PMC

Figure 1(A) Detail of patient’s photograph en face showing multiple pigmentary disorders of her light skin. The lips also show pigmentary disorders but the lip contour is not affected. The disease cannot be estimated from the external evaluation. (B) Oral inspection reveals clear mucous drooling after light compression of the upper lip (C) Close-up view of the oral aspect shown in (B) reveals the extended orifice of the labial minor salivary gland. (D) Expulsion of clear saliva after slight pressure on the lower lip from minor salivary glands of the lower lip vermilion during oral investigation for recurrent cheilitis glandularis. (E) After incision of the lower lip, berry-like enlarged minor salivary glands come to light.

Figure 1

Figure 3Immunohistochemical decoration of the interstitial lymphoid infiltrate (A: CD45, B: CD138). IgG4 staining showing a scattered pattern in (C), and very focal clustering in (D).

Figure 4